Diffuse cutaneous mastocytosis masquerading as linear IgA bullous dermatosis of childhood
نویسندگان
چکیده
منابع مشابه
IgA LINEAR BULLOUS DERMATOSIS IN CHILDHOOD
http://www.journal-imab-bg.org / J of IMAB. 2015, vol. 21, issue 4/ ABSTRACT: IgA linear bullous dermatosis, also known as chronic bullous dermatosis of childhood, is an autoimmune disease which may be idiopathic or drug-induced. The disease affects children and adults. We present a 4 years old girl with itchy polymorphic eruptions. The skin rash was presented by bullous-erosive rosette-like le...
متن کاملLinear IgA Bullous Dermatosis
Figure 1. Clinical photograph of linear IgA bullous dermatosis showing tense bullae and erosions involving the lower abdomen, inner thighs, and extremities.
متن کاملTreatment of linear IgA bullous dermatosis of childhood with flucloxacillin.
BACKGROUND Linear IgA bullous dermatosis of childhood is a rare autoimmune bullous disease that mainly affects preschool-aged children. Dapsone is considered the first-line therapy with prompt response from most patients. However, it may be contraindicated in certain conditions such as glucose-6-phosphate dehydrogenase deficiency. OBJECTIVE We sought to assess the efficacy of flucloxacillin i...
متن کاملChronic Bullous Disease or Linear IgA Dermatosis of Childhood -Revisited
Linear IgA dermatosis or chronic bullous disease of childhood (CBDC) is a nonhereditary, autoimmune subepidermal bullous disease, characterized by the presence of continuous linear deposits of IgA autoantibodies along the basement membrane zone. Antigens mainly involved in the pathogenesis of CBDC are a 97-kDa and a 120 –kDa protein, which represent fragments of the extracellular domain of coll...
متن کاملLinear IgA and IgG bullous dermatosis*
Childhood linear immunoglobulin A dermatosis is a rare autoimmune vesiculobullous disease. It results in linear deposition of autoantibodies (immunoglobulin A) against antigens in the basal membrane zone, leading to subepidermal cleavage. Additional depositions of immunoglobulin G and complement-3 might occur. It is still debated whether concomitant findings of immunoglobulins A and G should be...
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ژورنال
عنوان ژورنال: Dermatology Reports
سال: 2021
ISSN: 2036-7406,2036-7392
DOI: 10.4081/dr.2021.9021